Table 2. Diagnosis of incomplete presentation

AHA 2024 updated
Children with fever ≥ 5 days and 2 or 3 compatible clinical criteria OR infants with fever for ≥ 7 days without other explanationCompatible laboratory or echocardiographic findings• CRP ≥ 3.0 mg/dL and/or ESR ≥ 40 mm/hr• 3 or more laboratory findings 1) Anemia for age 2) Platelet count of ≥ 450,000 after the 7^th day of fever 3) Albumin ≤ 3.0 g/dL 4) Elevated ALT level 5) WBC count of ≥ 15,000 /mm³ 6) Urine ≥ 10 WBC /hpf• Z score of left anterior descending coronary artery or right coronary artery ≥ 2.5• Or ≥ 3 other suggestive features exist, including decreased left ventricular function, mitral regurgitation, pericardial effusion or Z scores in LAD or RCA of 2 to 2.5

AHA 2024 updated

Children with fever ≥ 5 days and 2 or 3 compatible clinical criteria OR infants with fever for ≥ 7 days without other explanationCompatible laboratory or echocardiographic findings• CRP ≥ 3.0 mg/dL and/or ESR ≥ 40 mm/hr• 3 or more laboratory findings 1) Anemia for age 2) Platelet count of ≥ 450,000 after the 7^th day of fever 3) Albumin ≤ 3.0 g/dL 4) Elevated ALT level 5) WBC count of ≥ 15,000 /mm³ 6) Urine ≥ 10 WBC /hpf• Z score of left anterior descending coronary artery or right coronary artery ≥ 2.5• Or ≥ 3 other suggestive features exist, including decreased left ventricular function, mitral regurgitation, pericardial effusion or Z scores in LAD or RCA of 2 to 2.5

JCS 2020
• The presence of 3 of 6 clinical features with coronary artery dilation and the exclusion of other febrile illnesses• The presence of 3 or 4 principal clinical features without coronary artery dilation but with features from the list of “Other significant clinical features”• Incomplete KD may be considered in the presence of ≤ 2 principle clinical features after excluding other diagnoses

JCS 2020

• The presence of 3 of 6 clinical features with coronary artery dilation and the exclusion of other febrile illnesses• The presence of 3 or 4 principal clinical features without coronary artery dilation but with features from the list of “Other significant clinical features”• Incomplete KD may be considered in the presence of ≤ 2 principle clinical features after excluding other diagnoses

AHA: American Heart Association; CRP: C-reactive protein; ESR: erythrocyte sedimentation rate; ALT: Alanine Aminotransferase; WBC: white blood cell; hpf: high power field; LAD: left anterior descending coronary artery; RCA: right coronary artery; JCS: Japanese Circulation Society; KD: Kawasaki disease.